Exploiting molecular biology for diagnosis and targeted management of pediatric low-grade gliomas

Document Type

Article

Abstract

The majority of brain tumors arising in children are low-grade gliomas. Although historically categorized together as pediatric low-grade gliomas (PLGGs), there is significant histologic and genetic diversity within this group. In general, prognosis for PLGGs is excellent, and limitation of sequelae from tumor and treatment is paramount. Advances in high-throughput genetic sequencing and gene expression profiling are fundamentally changing the way PLGGs are classified and managed. Here, we review the histologic subtypes and highlight how recent advances in elucidating the molecular pathogenesis of these tumors have refined diagnosis and prognostication. Additionally, we discuss how characterizing specific genetic alterations has paved the way for the rational use of targeted therapies that are currently in various phase clinical trials.

Publication Date

6-1-2016

Publication Title

Future Oncology

ISSN

14796694

E-ISSN

17448301

Volume

12

Issue

12

First Page

1493

Last Page

1506

PubMed ID

27072750

Digital Object Identifier (DOI)

10.2217/fon-2016-0039

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