Juvenile Intradural Chordoma: Case Report

Department

neurosurgery

Document Type

Article

Abstract

OBJECTIVE: We report the youngest known case of a prepontine intradural chordoma. These tumors are exceedingly rare. Unlike their more common extradural counterparts, no recurrence of an intradural chordoma has been reported. CLINICAL PRESENTATION: A 9-year-old boy underwent diagnostic imaging for evaluation of headaches. Although neurologically intact, a magnetic resonance imaging scan revealed a large prepontine mass with focal enhancement. INTERVENTION: Endoscopic-assisted gross total resection was attained with staged bilateral retrosigmoid approaches. There were no additional adjuvant therapies. At the time of the 1-year follow-up evaluation, the patient had no recurrence. CONCLUSION: By using an endoscopic-assisted procedure, we achieved complete resection of an intradural chordoma offering a potential for surgical cure. Resection is particularly advantageous because it spares the young child the need for radiation treatment. Close follow-up is warranted because we postulate that this tumor exists in a biological continuum between benign notochordal hamartomatous remnants and typical invasive chordomas. Copyright © by the Congress of Neurological Surgeons.

Publication Date

2008

Publication Title

Neurosurgery

ISSN

0148-396X

Volume

62

Issue

2

First Page

E525

Last Page

E526

Digital Object Identifier (DOI)

10.1227/01.neu.0000316022.74162.00

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