Cranioorbital fibrous dysplasia: with emphasis on visual impairment and current surgical management.
Document Type
Article
Abstract
Fibrous dysplasia is a benign but slowly progressive disorder of bone in which normal cancellous bone is replaced by immature woven bone and fibrous tissue. Significant deformity and both acute and chronic visual impairment can result. A contemporary understanding of fibrous dysplasia, emphasizing the origins of visual impairment, indications for decompressive surgery, and the techniques for correction of the cosmetic deformity are presented. In their experience and review of the literature, the authors found the most frequent clinical presentations to be exophthalmos, displacement of the globe, abnormalities of extraocular motility, cosmetic deformity, and visual impairment. Although traditionally the cause of visual impairment has been ascribed to impingement of the optic canal on the optic nerve, the authors' experience is that the most common cause of visual loss is cystic degeneration of the tumor, particularly with those involving the anterior clinoid process. Exophthalmos and optic canal stenosis are less common causes of visual impairment. Indications for surgical intervention include acute and/or serially radiographically documented and relentless visual impairment and significant cosmetic deformity. Individualized management strategies are also discussed.
Publication Date
1-1-2001
Publication Title
Neurosurgical focus
ISSN
1092-0684
E-ISSN
10920684
Volume
10
Issue
5
First Page
e6
PubMed ID
16724829
Digital Object Identifier (DOI)
10.3171/foc.2001.10.5.7
Recommended Citation
Dumont, A. S.; Boulos, P. T.; Jane, J. A.; Ellegala, D. B.; Newman, S. A.; and Jane, J. A., "Cranioorbital fibrous dysplasia: with emphasis on visual impairment and current surgical management." (2001). Neurosurgery. 1511.
https://scholar.barrowneuro.org/neurosurgery/1511