Hemimegalencephaly in a Patient With a Neurocutaneous Syndrome
Department
neurology
Document Type
Article
Abstract
A 5-year-old girl with a history of hypomelanosis of Ito and intractable epilepsy was evaluated for possible resective surgery. Magnetic resonance imaging showed an enlarged right hemisphere, whereas electrographic seizures were arising from the right hemisphere or had a generalized onset. The patient was believed to be a good candidate for hemispherectomy, but the family was hesitant and started a modified Atkins diet. Her seizure control has improved, but she continues to have weekly seizures. Hypomelanosis of Ito is a well-known cause of hemimegalencephaly and is often associated with intractable epilepsy and hemiparesis. Hemispherectomy can often be an effective treatment in intractable cases.
Medical Subject Headings
neurology
Publication Date
2008
Publication Title
Seminars in Pediatric Neurology
ISSN
1071-9091
Volume
15
Issue
4
First Page
190
Last Page
193
Digital Object Identifier (DOI)
10.1016/j.spen.2008.10.010
Recommended Citation
Chapman, Kevin and Cardenas, Javier F., "Hemimegalencephaly in a Patient With a Neurocutaneous Syndrome" (2008). Neurology. 37.
https://scholar.barrowneuro.org/neurology/37