Optic nerve head swelling in the Hadju-Cheney syndrome

Document Type

Article

Abstract

The Hadju-Cheney syndrome is one of the idiopathic acroosteolyses. Associated neurologic abnormalities are often a result of progressive basilar invagination. A 48-year-old man with the Hadju-Cheney syndrome developed progressive bilateral visual loss. On examination, he had hyperopia, choroidal folds, optic nerve head swelling, and mild optic neuropathy. Computed tomographic scans showed massive enlargement of both intraorbital optic nerve sheaths. Improvement occurred after optic nerve sheath fenestration. Visual loss due to optic nerve meningocele can occur in the Hadju-Cheney syndrome. Optic nerve sheath fenestration can result in visual improvement. It is unclear whether the occurrence of optic nerve meningocele is causally or fortuitously related to the Hadju-Cheney syndrome.

Medical Subject Headings

Fundus Oculi; Humans; Male; Middle Aged; Optic Disk (pathology); Optic Nerve (pathology, surgery); Osteolysis, Essential (complications, diagnostic imaging, pathology); Papilledema (complications, pathology); Syndrome; Tomography, X-Ray Computed; Vision Disorders (etiology); Visual Acuity; Visual Fields

Publication Date

3-1-1998

Publication Title

Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society

ISSN

1070-8022

Volume

18

Issue

1

First Page

60

Last Page

5

PubMed ID

9532545

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