A Randomized Placebo-Controlled Double-Blind Phase IIb Trial Evaluating the Safety and Efficacy of Tirasemtiv in Patients With Amyotrophic Lateral Sclerosis
Department
neurology
Document Type
Article
Abstract
Our objectives were to evaluate the safety and tolerability of tirasemtiv over 12 weeks and its effect on the revised ALS Functional Rating Scale (ALSFRS-R) and other secondary functional measures. This randomized, double-blind, placebo-controlled trial enrolled adults with ALS and slow vital capacity (SVC) > 50% from 73 centers in eight countries. Patients who tolerated open-label tirasemtiv 125 mg b.i.d. for one week were randomized to double-blind treatment either to placebo or tirasemtiv, escalating to a maximum tolerated dose up to 250 mg b.i.d. The primary endpoint was the change from baseline in ALSFRS-R; secondary endpoints included SVC, maximum voluntary ventilation, sniff nasal inspiratory pressure, isometric muscle strength, and sub-maximum handgrip fatigue. Of 711 patients enrolled, 596 were randomized and received at least one dose of double-blind treatment. The primary endpoint showed no treatment effect (tirasemtiv: ˆ’2.98 ± 0.28, placebo: ˆ’2.40 ± 0.25, p = 0.114); however, SVC and muscle strength declined significantly more slowly on tirasemtiv (95% CI p = 0.0006, p = 0.0158, respectively). Dropouts and serious adverse events occurred more frequently in the tirasemtiv group. In conclusion, this was a negative study with respect to the primary endpoint; however, the effects on SVC and muscle strength suggest a potentially important effect of tirasemtiv warranting further evaluation over a longer period in ALS.
Medical Subject Headings
neurology
Publication Date
2016
Publication Title
Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration
ISSN
2167-8421
Volume
17
Issue
43591
First Page
426
Last Page
435
Digital Object Identifier (DOI)
10.3109/21678421.2016.1148169
Recommended Citation
Shefner, Jeremy M.; Wolff, Andrew A.; Meng, Lisa; Bian, Amy; Lee, Jacqueline; Barragan, Donna; and Andrews, Jinsy A., "A Randomized Placebo-Controlled Double-Blind Phase IIb Trial Evaluating the Safety and Efficacy of Tirasemtiv in Patients With Amyotrophic Lateral Sclerosis" (2016). Neurology. 157.
https://scholar.barrowneuro.org/neurology/157